SEOM-GEIS Spanish clinical guidelines for the management of soft‑tissue sarcomas (2024)

Other authors

Institut Català de la Salut

[Serrano C] Servei d’Oncologia Mèdica, Vall d’Hebron Hospital Universitari, Barcelona, Spain. [Arregui M] Servicio de Oncología Médica, Hospital General, Universitario Gregorio Marañón, Madrid, Spain. [Carrasco I] Servicio de Oncología Médica Hospital, Universitario Virgen del Rocío, Seville, Spain. [Hindi N] Servicio de Oncología Médica Fundación Jiménez Díaz, Madrid, Spain. [Martínez Trufero J] Servicio de Oncología Médica Hospital Universitario Miguel Servet, Saragossa, Spain. [Martínez García J] Servicio de Oncología Médica Hospital, Universitario Virgen de La Arrixaca, Murcia, Spain

Vall d'Hebron Barcelona Hospital Campus

Publication date

2025-04-25T09:46:42Z

2025-04-25T09:46:42Z

2025-04



Abstract

Rare cancer; Sarcoma; Soft-tissue sarcoma


Cáncer raro; Sarcoma; Sarcoma de tejidos blandos


Càncer rar; Sarcoma; Sarcoma de teixits tous


Soft-tissue sarcomas are rare, diverse malignant tumors of mesenchymal origin, requiring diagnosis and treatment by a specialized multidisciplinary team. Initial assessment includes radiology and biopsy, followed by wide surgical resection with clear margins for localized cases. Radiotherapy is recommended for large, deep, high-grade tumors or after incomplete resection, while perioperative chemotherapy may be considered for high-risk cases. In oligometastatic disease, combining local and systemic therapies is an option. Anthracycline-based chemotherapy is the first-line treatment in advanced disease, though other drugs show efficacy in certain subtypes. Given the limited options, enrolling in clinical trials is advised for patients needing further treatment.

Document Type

Article


Published version

Language

English

Publisher

Springer

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Attribution 4.0 International

http://creativecommons.org/licenses/by/4.0/

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