Institut Català de la Salut
[Serrano C] Servei d’Oncologia Mèdica, Vall d’Hebron Hospital Universitari, Barcelona, Spain. [Arregui M] Servicio de Oncología Médica, Hospital General, Universitario Gregorio Marañón, Madrid, Spain. [Carrasco I] Servicio de Oncología Médica Hospital, Universitario Virgen del Rocío, Seville, Spain. [Hindi N] Servicio de Oncología Médica Fundación Jiménez Díaz, Madrid, Spain. [Martínez Trufero J] Servicio de Oncología Médica Hospital Universitario Miguel Servet, Saragossa, Spain. [Martínez García J] Servicio de Oncología Médica Hospital, Universitario Virgen de La Arrixaca, Murcia, Spain
Vall d'Hebron Barcelona Hospital Campus
2025-04-25T09:46:42Z
2025-04-25T09:46:42Z
2025-04
Rare cancer; Sarcoma; Soft-tissue sarcoma
Cáncer raro; Sarcoma; Sarcoma de tejidos blandos
Càncer rar; Sarcoma; Sarcoma de teixits tous
Soft-tissue sarcomas are rare, diverse malignant tumors of mesenchymal origin, requiring diagnosis and treatment by a specialized multidisciplinary team. Initial assessment includes radiology and biopsy, followed by wide surgical resection with clear margins for localized cases. Radiotherapy is recommended for large, deep, high-grade tumors or after incomplete resection, while perioperative chemotherapy may be considered for high-risk cases. In oligometastatic disease, combining local and systemic therapies is an option. Anthracycline-based chemotherapy is the first-line treatment in advanced disease, though other drugs show efficacy in certain subtypes. Given the limited options, enrolling in clinical trials is advised for patients needing further treatment.
Article
Published version
English
Sarcoma; Tumors de parts toves - Tractament; Tumors de parts toves - Diagnòstic; DISEASES::Neoplasms::Neoplasms by Site::Soft Tissue Neoplasms; Other subheadings::Other subheadings::/therapy; DISEASES::Neoplasms::Neoplasms by Site::Soft Tissue Neoplasms; Other subheadings::Other subheadings::/diagnosis; DISEASES::Neoplasms::Neoplasms by Histologic Type::Neoplasms, Connective and Soft Tissue::Sarcoma; ENFERMEDADES::neoplasias::neoplasias por localización::neoplasias de los tejidos blandos; Otros calificadores::Otros calificadores::/terapia; ENFERMEDADES::neoplasias::neoplasias por localización::neoplasias de los tejidos blandos; Otros calificadores::Otros calificadores::/diagnóstico; ENFERMEDADES::neoplasias::neoplasias por tipo histológico::neoplasias de tejido conjuntivo y de tejidos blandos::sarcoma
Springer
Clinical and Translational Oncology;27
https://doi.org/10.1007/s12094-024-03842-5
Attribution 4.0 International
http://creativecommons.org/licenses/by/4.0/
Articles científics - HVH [3440]